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Characteristics

 

Most likely features

 

  • Developmental delay
  • Recognisable facial appearance
  • Learning difficulty or disability
  • Low muscle tone, so babies and children feel floppy
 

 

Other common features 

 

  • Heart conditions
  • Seizures
  • Minor genital anomalies in males
  • Sleep difficulties
  • Behaviour difficulties
  • Strabismus (squint) or other unusual eye features
  • Respiratory infections caused by aspiration reflux/GERD.


 

Less common features 

 

  • Slightly unusual hands and/or feet (single palm crease, incurving fingers, short or tapering fingers, unusually positioned feet)
  • Hearing impairment
  • Kidney anomalies
  • Connective tissue disorders, including lax joints and hernias
  • Patches of lighter skin colouring
  • Dental anomalies 
  • Anal atresia (the normal opening for the anus is not present)
  • Possibly, overweight

 


Information reproduced with permission, from Unique's Kleefstra syndrome leaflet.

   

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